Mitochondrial ROS produced via reverse electron transport extend animal lifespan F Scialo, A Sriram, D Fernandez-Ayala, N Gubina, M Lohmus, G Nelson, ... Cell metabolism 23 (4), 725-734, 2016 | 351 | 2016 |
In vivo functional analysis of the human mitochondrial DNA polymerase POLG expressed in cultured human cells JN Spelbrink, JM Toivonen, GAJ Hakkaart, JM Kurkela, HM Cooper, ... Journal of Biological Chemistry 275 (32), 24818-24828, 2000 | 230 | 2000 |
Mitochondrial nucleoid interacting proteins support mitochondrial protein synthesis J He, HM Cooper, A Reyes, M Di Re, H Sembongi, TR Litwin, J Gao, ... Nucleic acids research 40 (13), 6109-6121, 2012 | 220 | 2012 |
The human SIRT3 protein deacetylase is exclusively mitochondrial HM Cooper, JN Spelbrink Biochemical Journal 411 (2), 279-285, 2008 | 155 | 2008 |
Infantile-onset spinocerebellar ataxia and mitochondrial recessive ataxia syndrome are associated with neuronal complex I defect and mtDNA depletion AH Hakonen, S Goffart, S Marjavaara, A Paetau, H Cooper, K Mattila, ... Human molecular genetics 17 (23), 3822-3835, 2008 | 151 | 2008 |
Twinkle mutations associated with autosomal dominant progressive external ophthalmoplegia lead to impaired helicase function and in vivo mtDNA … S Goffart, HM Cooper, H Tyynismaa, S Wanrooij, A Suomalainen, ... Human molecular genetics 18 (2), 328-340, 2009 | 150 | 2009 |
Human mitochondrial DNA-protein complexes attach to a cholesterol-rich membrane structure JM Gerhold, Ş Cansiz-Arda, M Lõhmus, O Engberg, A Reyes, ... Scientific reports 5 (1), 15292, 2015 | 107 | 2015 |
Human C4orf14 interacts with the mitochondrial nucleoid and is involved in the biogenesis of the small mitochondrial ribosomal subunit J He, HM Cooper, A Reyes, M Di Re, L Kazak, SR Wood, CC Mao, ... Nucleic acids research 40 (13), 6097-6108, 2012 | 99 | 2012 |
ATPase-deficient mitochondrial inner membrane protein ATAD3A disturbs mitochondrial dynamics in dominant hereditary spastic paraplegia HM Cooper, Y Yang, E Ylikallio, R Khairullin, R Woldegebriel, KL Lin, ... Human molecular genetics 26 (8), 1432-1443, 2017 | 85 | 2017 |
A new splice variant of the mouse SIRT3 gene encodes the mitochondrial precursor protein HM Cooper, JY Huang, E Verdin, JN Spelbrink PloS one 4 (3), e4986, 2009 | 62 | 2009 |
Mitochondrial antibodies in primary biliary cirrhosis: IV. Significance of membrane structure for the complement-fixing antigen PA Berg, IM Roitt, D Doniach, HM Cooper Immunology 17 (2), 281, 1969 | 48 | 1969 |
Sphingosine kinase 1 overexpression induces MFN2 fragmentation and alters mitochondrial matrix Ca2+ handling in HeLa cells I Pulli, C Löf, T Blom, MY Asghar, T Lassila, N Bäck, KL Lin, JH Nyström, ... Biochimica et Biophysica Acta (BBA)-Molecular Cell Research 1866 (9), 1475-1486, 2019 | 14 | 2019 |
Severe neonatal MEGDHEL syndrome with a homozygous truncating mutation in SERAC1 V Fellman, R Banerjee, KL Lin, I Pulli, H Cooper, H Tyynismaa, J Kallijärvi Biochimica et Biophysica Acta (BBA)-Molecular Basis of Disease 1868 (1), 166298, 2022 | 5 | 2022 |
ATPase-deficient ATAD3A alters mitochondrial dynamics in hereditary spastic paraplegia RA Woldegebriel, HM Cooper, EA Ylikallio, R Khairullin, K Lin, L Euro, ... European Journal of Human Genetics 26, 111-112, 2018 | | 2018 |
Regulating mitochondrial function: The roles of SIRT3 as a mitochondrial protein deacetylase and the functions of the Twinkle helicase in mitochondrial DNA maintenance H Cooper Tampere University Press, 2009 | | 2009 |
Twinkle mutations associated with autosomal dominant progressive external ophthalmoplegia lead to impaired helicase function and in vivo mtDNA replication stalling. S Goffart, HM Cooper, H Tyynismaa, S Wanrooij, A Suomalainen, ... | | 2008 |
BBA-Molecular Basis of Disease V Fellman, R Banerjee, KL Lin, I Pulli, H Cooper, H Tyynismaa, J Kallijärvi | | |
ATpase-deficient mitochondrial inner membrane protein ATAD3a disturbs mitochondrial dynamics in dominant hereditary spastic paraplegia R Khairullin, L Euro, R Woldegebriel, S Kaakkola, K Lin, E Ylikallio, ... | | |